Atypical Caroli's Syndrome: A Case Report with Absent 'Central Sign'

Thank you for your kind words. It is understandable that your understanding of CS syndrome comes primarily from publications and literature, given its rarity. It is important to note that the fibrosis associated with CS syndrome can indeed cause the "central sign" to disappear in radiological examinations. In this particular case, since there were no intrahepatic cystic changes or biliary dilatation observed, and the "central point sign" was also absent, it is appropriate to describe it as an "atypical CS." It is crucial to continue researching and learning about rare diseases like CS syndrome to enhance our understanding and improve diagnosis and treatment approaches.