三羧酸循环相关蛋白:

  1. 柠檬酸合成酶(Citrate Synthase,CS)- CS,citrate synthase
  2. 苹果酸脱氢酶(Isocitrate Dehydrogenase,IDH)- IDH,isocitrate dehydrogenase
  3. 甲酰基转移酶(Malate Dehydrogenase,MDH)- MDH,malate dehydrogenase

呼吸链相关蛋白:

  1. NADH脱氢酶(NADH Dehydrogenase)- ND, NADH dehydrogenase
  2. 细胞色素c氧化酶(Cytochrome c Oxidase)- COX, cytochrome c oxidase
  3. ATP合酶(ATP Synthase)- ATP5, ATP synthase

线粒体DNA相关蛋白:

  1. 线粒体DNA聚合酶(Mitochondrial DNA Polymerase)- POLG, mitochondrial DNA polymerase
  2. 线粒体DNA拆分酶(Mitochondrial DNA Helicase)- TWNK, mitochondrial DNA helicase

线粒体膜相关蛋白:

  1. 转膜蛋白(Translocase)- TIM, translocase of inner mitochondrial membrane
  2. 电子传递蛋白(Electron Transfer Protein)- ETF, electron transfer flavoprotein
  3. 线粒体内膜通道蛋白(Mitochondrial Inner Membrane Protein)- MIC, mitochondrial inner membrane protein
线粒体蛋白列表:三羧酸循环、呼吸链、DNA及膜相关蛋白

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